7.1.3 Headache attributed to intracranial hypertension secondary to hydrocephalus

Description:
Headache caused by hydrocephalus, acompanied by other symptoms and/or clinical signs of increased cerebrospinal fluid pressure or hydrocephalus. It remits after resolution of the hydrocephalus.

Diagnostic criteria:
A. Any headache fulfilling criterion C
B. Hydrocephalus has been diagnosed, with CSF pressure >250 mm CSF (measured by lumbar puncture performed in the lateral decubitus position, without sedative medications or by epidural or intraventricular monitoring)
C. Evidence of causation demonstrated by either or both of the following:

    1. headache has developed in temporal relation to the hydrocephalus
    2. either or both of the following:

      a) headache has significantly worsened in parallel with worsening of the hydrocephalus
      b) headache has significantly improved in parallel with improvement in the hydrocephalus

D. Not better accounted for by another ICHD-3 diagnosis.

Comment:
Normal-pressure hydrocephalus usually does not cause headache; occasionally, mild dull headache is reported.