6.5 Headache attributed to cervical carotid or vertebral artery disorder

Headache and/or pain in the face and/or neck caused by non-inflammatory lesions affecting the cervical carotid and/or vertebral arteries. The pain generally has a sudden (even thunderclap) onset. It can remain isolated or be a warning symptom preceding the focal deficits of ischaemic stroke.

Diagnostic criteria:
A. Any new headache and/or facial or neck pain fulfilling criterion C
B. A cervical artery lesion has been demonstrated, or a surgical or radiological intervention has been performed on a cervical artery
C. Evidence of causation demonstrated by at least two of the following:

    1. pain has developed in close temporal relation to other local signs of cervical artery disorder, or has led to the diagnosis of cervical artery disorder
    2. either or both of the following:

      a) pain has significantly worsened in parallel with other signs of the cervical artery lesion
      b) pain has significantly improved or resolved within 1 month of its onset

    3. pain is unilateral and ipsilateral to the affected cervical artery

D. Not better accounted for by another ICHD-3 diagnosis.